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45-årig kvinna söker för tilltagande svaghet i benen och "muskelömhet". Hon beskriver svårigheter att resa sig upp från TV-soffan och gå i trappor, hon har också märkt svaghet i armarna när hon borstar håret. I status finner man muskelsvaghet i nackreflektorer, samt i proximala extremitetsmuskler. a) Förstahandsdiagnos?
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